👉 Kynuria is a rare genetic disorder that affects the kidneys. It results from an abnormality in the production of kynurenines, which are a type of amino acid found in the urine. These substances are essential for maintaining proper kidney function and can cause problems if they accumulate too much. The exact causes of kynuria are not fully understood, but it is thought to be caused by mutations in genes that regulate the production of kynurine. The disorder can affect both males and